tailieunhanh - Báo cáo y học: "Undifferentiated liver sarcoma – rare entity: a case report and review of the literature"

Tuyển tập báo cáo các nghiên cứu khoa học quốc tế ngành y học dành cho các bạn tham khảo đề tài: Undifferentiated liver sarcoma – rare entity: a case report and review of the literature. | Journal of Medical Case Reports BioMed Central Open Access Case report Undifferentiated liver sarcoma - rare entity a case report and review of the literature Kashif Iqbal 1 Zhang Meng Xian2 and Chen Yuan2 Address Nuclear Medicine Oncology and Radiotherapy Institute G-8 3 Islamabad Pakistan and 2Cancer Center Tongji Hospital Tongji Medical College. Huazhong University of Science and Technology. Wuhan. China Email Kashif Iqbal - kashifrajput@ ZhangMengXian-zhangmengxian@ Chen Yuan - chenyuan008@ Corresponding author Published 25 January 2008 Received 23 December 2006 Journal of Medical Case Reports 2008 2 20 doi 1752-1947-2-20 Accepted 25 January 2008 This article is available from http content 2 1 20 2008 Iqbal et al licensee BioMed Central Ltd. This is an Open Access article distributed under the terms of the Creative Commons Attribution License http licenses by which permits unrestricted use distribution and reproduction in any medium provided the original work is properly cited. Abstract_ Introduction Undifferentiated Liver Sarcoma also known as Undifferentiated Embryonal Sarcoma of the Liver is a rare highly malignant neoplasm which affects mostly the pediatric population although a few cases have been reported in adults. It accounts for about 13 of pediatric hepatic malignancies. Case presentation We report a case of undifferentiated liver sarcoma in a 14-year-old Chinese boy who presented with non-specific right hypochondriac pain. Exploratory laparotomy with tumor resection was performed followed by adjuvant chemotherapy. Conclusion Undifferentiated Liver Sarcoma is a rare highly malignant hepatic neoplasm affecting almost exclusively the pediatric population. The prognosis is poor but recent evidence shows that long-term survival is possible after complete surgical resection and .