tailieunhanh - Báo cáo y học: " Right pulmonary artery agenesis presenting with uncontrolled asthma in an adult: a case report"

Tuyển tập báo cáo các nghiên cứu khoa học quốc tế ngành y học dành cho các bạn tham khảo đề tài: Right pulmonary artery agenesis presenting with uncontrolled asthma in an adult: a case report. | Hayek et al. Journal of Medical Case Reports 2011 5 353 http content 5 1 353 JOURNALOF medical case reports CASE REPORT Open Access Right pulmonary artery agenesis presenting with uncontrolled asthma in an adult a case report Hafez Hayek Jaime Palomino and Supat Thammasitboon Abstract Introduction Unilateral absence of the pulmonary artery UAPA or pulmonary artery agenesis is a rare congenital disorder presenting with a wide spectrum of symptoms. The clinical presentation is variable and many patients can be asymptomatic for many years and even throughout their lives. Case presentation We report the case of a 53-year-old African-American woman who was diagnosed with right pulmonary artery agenesis after presenting with uncontrolled asthma and recurrent bronchopulmonary infections. Conclusion In an unexplained case of recurrent respiratory infections and shortness of breath the possibility of a rare congenital anomaly like UAPA should be considered and an appropriate evaluation should be done. Introduction Unilateral absence of the pulmonary artery UAPA or pulmonary artery agenesis is a rare congenital disorder presenting with a wide spectrum of symptoms. The first case was reported in 1868. The prevalence of isolated UAPA is estimated to be around 1 in 200 000 individuals 1 . The clinical presentation is variable and many patients may be asymptomatic for many years and even throughout their lives. Recurrent pulmonary infections decreased exercise tolerance and shortness of breath on exertion are the most common symptoms. In a literature review by Ten Harkel et al. 2 recurrent pulmonary infections were present in 37 of cases dyspnea or exercise limitations in 40 hemoptysis in 20 and high-altitude pulmonary edema in 12 . Pulmonary hypertension was found in 44 of patients which is higher than a previous report of 20-25 3 4 . Case presentation A 53-year-old African-American woman was referred to our pulmonary clinic because of uncontrolled .