tailieunhanh - Báo cáo y học: "Long term follow up after surgery in congenitally corrected transposition of the great arteries with a right ventricle in the systemic circulation"

Tuyển tập các báo cáo nghiên cứu về y học được đăng trên tạp chí y học Wertheim cung cấp cho các bạn kiến thức về ngành y đề tài: Long term follow up after surgery in congenitally corrected transposition of the great arteries with a right ventricle in the systemic circulation. | Bogers et al. Journal of Cardiothoracic Surgery 2010 5 74 http content 5 1 74 JOTS JOURNAL OF CARDIOTHORACIC SURGERY RESEARCH ARTICLE Open Access Long term follow up after surgery in congenitally corrected transposition of the great arteries with a right ventricle in the systemic circulation Ad JJC Bogers1 Stuart J Head1 Peter L de Jong1 Maarten Witsenburg2 3 Arie Pieter Kappetein1 Abstract Aim of the study To investigate the long-term outcome of surgical treatment for congenitally corrected transposition of the great arteries CCTGA in patients with biventricular repair with the right ventricle as systemic ventricle. Methods A total of 32 patients with CCTGA were operated between January 1972 and October 2008. These operations comprised 18 patients with a repair with a normal left ventricular outflow tract 11 patients with a Rastelli repair of the left ventricle to the pulmonary artery and 3 patients with a cardiac transplantation. Results Excluding the cardiac transplantation patients mean age at operation was 16 years sd 15 years range 1 week - 49 years . Median follow-up was 12 years sd 10 years range 7 days - 32 years . Survival obtained from Kaplan-Meier analysis at 20 years after surgery was 63 CI 53-73 . For the non-Rastelli group these data at 20 years were 62 CI 48-76 and for the Rastelli group 67 CI 51-83 . Freedom of reoperation at 20 years was 32 CI 19-45 in the overall group. In the non-Rastelli group the data at 20 years were 47 CI 11-83 and for the Rastelli group 21 CI 0-54 after almost 19 years. Conclusions Long term follow up confirms that surgery in CCTGA with the right ventricle as systemic ventricle has a suboptimal survival and limited freedom of reoperation. Death occurred mostly as a result of cardiac failure. Background Congenitally corrected transposition of the great arteries CCTGA is a rare cardiac anomaly with an incidence of less than 1 of patients with congenital heart disease 1 . Characteristically the .