tailieunhanh - Pompe disease in children and adults: natural course, disease severity and impact on daily life

The transition from efficacy of interventions to effectiveness of delivery strategies is where we so often lose our way. If efficacy is “proven” by techniques such as the randomized controlled trial that screen out the noise of confounding variables, then, ultimately, the techniques to assess effectiveness of delivery strategies and to decide priorities for health sector policy must do just the opposite. They must take into account, they must even grow out of, precisely the messy, contradictory, dissonant noises of real life. In this sense “delivery strategy” is a misleading term,. | ompe disease in children and adults natural course disease severity and impact on daily life Results from an international patient survey Pompe disease in children and adults natural course disease severity and impact on daily life Results from an international patient survey Marloes Hagemans The studies described in this thesis were performed at Erasmus MC University Medical Center Rotterdam the Netherlands and were financially supported by the Princess Beatrix Fund the International Pompe Association and Genzyme Corp. Boston MA. The printing of this thesis was sponsored by Genzyme Europe . and the International Pompe Association. ISBN 90-9020644-2 . Hagemans 2006 All rights reserved. No part of this thesis may be reproduced stored in a retrieval system or transmitted in any form or by any means without the prior written permission of the author. The copyright of the publications remains with the publishers. Layout Tom de Vries Lentsch Cover photography Peter Nicolai Cover design Lennart Nicolai Tom de Vries Lentsch Printed by PrintPartners Ipskamp .

• Sức khỏe trẻ em
• Establishment
• Biogeographic Areas
• Distributing Endemic
• Dominican Republic
• Biogeography
• Intertidal Barnacles
• Crop establishment methods
• Grain yield
• Different crop establishment methods
• Yield attributes
• Establishment method
• Drum seeder
• Direct seeded rice
• Aerobic rice
• Dry seeded condition
• Rice establishment methods
• Weed management
• Weed dynamics
• Various weed management approaches
• Weed dynamics in rice
• The establishment of venture capital funds
• Venture capital funds for technology innovation activities
• Technology innovation activities in Vietnam
• Venture capital fund
• Crop establishment
• Direct seeding
• Late sown rice
• Different establishment methods
• Rice under puddle condition
• Enhancing productivity
• Nutrient uptake
• Establishment methods and varieties
• Kharif finger millet
• Millet (Eleusine coracana (L ) Gaertn )
• Varieties on yield
• Weed dynamics in rice crop
• Various crop establishment methods
• Weed management approaches
• Residue on yield
• Yield attributes and economics
• Economics of ricein RW system
• Northern plains of IGP
• Establishment methods
• Economics of rice
• Weed management practices
• Maize performance
• The establishment
• Mathematics
• Physics
• Scientific reports
• scientific studies
• natural sciences
• Tạp chí khoa học
• Tạp chí Công nghệ
• Quản lí công nghệ
• The KIST in South Korea
• Establishment of the V KIST in Vietnam
• Vietnam Journal of Mechanics
• Analytical approach to analyze nonlinear dynamic response
• Eccentrically stiffened functionally graded circular cylindrical shells subjected
• Dependent axial compression and external pressure
• Governing equations establishment
• Functionally graded materia
• On a form of lyapunov exponents
• Establishment of the form
• The disturbance direction
• The disturbance norm
• Types of momentum defect diffusion
• The begining of the wake and wake establishment zone
• The coupled wake and comparison
• The isolated wake
• Entrepreneurship development
• Value addition
• Empowerment of rural women
• Establishment of entrepreneurial activities
• Nutrition knowledge
• Kunkuni joha
• Amona bao
• Black rice and jhengoni bora
• Methods of establishment
• Biological properties
• Nitrogen management
• Field experiment
• Assessment of energetics
• Rice with irrigation
• Nitrogen management practices
• Nutrient management
• Yield and economics
• Kharif rice (Oryza sativa L
• Nutrient management on yield
• Economics of Kharif rice
• African marigold
• French marigold
• Nodal segment
• Culture establishment
• Micro shoots in African
• French marigold genotypes
• Water use efficiency
• Rice genotypes
• Different rice establishment methods
• Different growing environment
• Micropot technique
• Performance of sunflower
• Influenced by establishment technique
• College of agriculture
• Direct wet seeded
• Weed management practices on rice
• Yield and economic impact
• In vitro sterilization protocol
• Establishment of litchi
• Litchi (Litchi chinensis Sonn) cv Purbi
• Varying concentrations
• Crop difficult to propagate
• Sweet corn
• Sweet corn hybrid
• Temperate conditions