tailieunhanh - Báo cáo y học: "Single ventricle with persistent truncus arteriosus as two rare entities in an adult patient: a case report"

Tuyển tập báo cáo các nghiên cứu khoa học quốc tế ngành y học dành cho các bạn tham khảo đề tài: Single ventricle with persistent truncus arteriosus as two rare entities in an adult patient: a case report | Journal of Medical Case Reports BioMed Central Open Access Case report Single ventricle with persistent truncus arteriosus as two rare entities in an adult patient a case report Inna Porter and James Vacek Address University of Kansas Hospital Rainbow Boulevard Kansas City KS 66160 USA Email Inna Porter - iporter@ James Vacek - jlvacek@ Corresponding author Published 30 May 2008 Received 13 February 2007 Journal of Medical Case Reports 2008 2 184 doi 1752-1947-2-184 Accepted 30 May 2008 This article is available from http content 2 1 184 2008 Porter and Vacek licensee BioMed Central Ltd. This is an Open Access article distributed under the terms of the Creative Commons Attribution License http licenses by which permits unrestricted use distribution and reproduction in any medium provided the original work is properly cited. Abstract Introduction Single ventricle and truncus arteriosus are both rare congenital cardiac syndromes with limited survival. Their occurrence together is extremely uncommon and prolonged survival is exceptionally rare. We present the case of a patient who had both of these defects with survival to age 45. Case presentation We describe the vase of a 45-year-old man with the unusual occurrence of two very rare congenital cardiac defects. He was found to have both truncus arteriosus and single ventricle with long survival. His history clinical course and anatomic findings are discussed along with the factors which may have contributed to his longevity which is unique in the medical literature. His management reflected the state of medical knowledge at the time when he presented and although alternate approaches may have been utilized if the patient presented today this case does indicate the efficacy of the management options available at the time and place of the patient s contacts with the medical care system in Belarus. We discuss the findings frequency classification .