tailieunhanh - Báo cáo y học: "Primitive neuroectodermal tumour of the kidney with vena caval and atrial tumour thrombus: a case report"

Tuyển tập báo cáo các nghiên cứu khoa học quốc tế ngành y học dành cho các bạn tham khảo đề tài: Primitive neuroectodermal tumour of the kidney with vena caval and atrial tumour thrombus: a case report | Journal of Medical Case Reports BioMed Central Open Access Case report Primitive neuroectodermal tumour of the kidney with vena caval and atrial tumour thrombus a case report Poh Ho Ong1 Ramaswamy Manikandan 1 Joe Philip1 Kirsten Hope2 and Eric PM Williamson1 Address Department of Urology University Hospital Aintree Liverpool L9 7AL UK and 2Department of Pathology Royal Liverpool University Hospital Liverpool L7 8XP UK Email Poh Ho Ong - catphong@ Ramaswamy Manikandan - armanikan2000@ Joe Philip - Indianajoe@ Kirsten Hope - Eric PM Williamson - Corresponding author Published II August 2008 Received 19 December 2007 Journal of Medical Case Reports 2008 2 265 doi 1752-1947-2-265 Accepted 11 August 2008 This article is available from http content 2 1 265 2008 Ong et al licensee BioMed Central Ltd. This is an Open Access article distributed under the terms of the Creative Commons Attribution License http licenses by which permits unrestricted use distribution and reproduction in any medium provided the original work is properly cited. Abstract Introduction Renal primitive neuroectodermal tumour is an extremely rare malignancy. Case presentation A 21-year-old woman presented with microscopic haematuria a palpable right loin mass dyspnoea dizziness and fatigue. Initial ultrasound scan of the kidneys revealed an 11 cm right renal mass with venous extension into the inferior vena cava. Computed tomography of the thorax and abdomen revealed an extension of the large renal mass into the right renal vein inferior vena cava and up to the right atrium. A small paracaval lymph node was noted and three small metastatic nodules were identified within the lung parenchyma. The patient underwent a radical nephrectomy and inferior vena caval tumour level IV thrombectomy with cardiopulmonary bypass and deep hypothermic circulatory arrest. .