tailieunhanh - Báo cáo y học: " Sclerosing epithelioid fibrosarcoma as a rare cause of ascites in a young man: a case report"

Tuyển tập báo cáo các nghiên cứu khoa học quốc tế ngành y học dành cho các bạn tham khảo đề tài: Sclerosing epithelioid fibrosarcoma as a rare cause of ascites in a young man: a case report | Journal of Medical Case Reports BioMed Central Open Access Case report Sclerosing epithelioid fibrosarcoma as a rare cause of ascites in a young man a case report Philip J Smith Beverley Almeida Jasna Krajacevic and Barry Taylor Address North Cheshire NHS Trust Warrington Hospital Cheshire WA5 1QG UK Email Philip J Smith - pjsmith@ BeverleyAlmeida-beverleyalmeida@ Jasna Krajacevic - kozarevic@ Barry Taylor - Corresponding author Published 25 July 2008 Received 4 January 2008 Journal of Medical Case Reports 2008 2 248 doi 1752-1947-2-248 Accepted 25 July 2008 This article is available from http content 2 1 248 2008 Smith et al licensee BioMed Central Ltd. This is an Open Access article distributed under the terms of the Creative Commons Attribution License http licenses by which permits unrestricted use distribution and reproduction in any medium provided the original work is properly cited. Abstract_ Introduction Sclerosing epithelioid fibrosarcoma is a rare but distinct variant of fibrosarcoma that not only presents as a deep-seated mass on the limbs and neck but can also occur adjacent to the fascia or peritoneum as well as the trunk and spine. We report the case of an intra-abdominal sclerosing epithelioid fibrosarcoma which to best of the authors knowledge has not been described previously. The patient discussed here developed lung metastases but is still alive 1-year post-diagnosis. Case presentation A 29-year-old man presented with a 2-week history of progressive abdominal distension and pain and was found to have marked ascites. A full liver screen was unremarkable with abdominal and chest computed tomography scans only confirming ascites. After a diagnostic laparotomy biopsies were taken from the greater omentum and peritoneal nodules. Histopathology .